The prevalence of bronchiectasis in patients with Marfan syndrome

H. S. Hwang; C. A. Yi; H. Yoo; J. H. Yang; D. K. Kim; Won Jung Koh

doi:10.5588/ijtld.13.0763

The prevalence of bronchiectasis in patients with Marfan syndrome

H. S. Hwang
, C. A. Yi
, H. Yoo
, J. H. Yang
, D. K. Kim
, Won Jung Koh

Sungkyunkwan University

Research output: Contribution to journal › Article › peer-review

16 Scopus citations

Abstract

An association has been suggested between Marfan syndrome (MFS) and the nodular bronchiectatic form of lung disease caused by non-tuberculous mycobacteria (NTM). We evaluated the prevalence of bronchiectasis in 79 adult patients with MFS using computed tomography (CT) imaging. Airway dilation indicative of bronchiectasis (22/79, 28%) and bronchioloectasis (10/79, 13%) were relatively common, although the extent of dilation was not severe and was frequently confined to a single lobe. However, bronchiolitis was evident in only three patients (4%), and no patient was diagnosed with NTM lung disease.

Original language	English
Pages (from-to)	995-997
Number of pages	3
Journal	International Journal of Tuberculosis and Lung Disease
Volume	18
Issue number	8
DOIs	https://doi.org/10.5588/ijtld.13.0763
State	Published - 1 Aug 2014
Externally published	Yes

UN SDGs

This output contributes to the following UN Sustainable Development Goals (SDGs)

SDG 3 Good Health and Well-being

Keywords

Bronchiectasis
Marfan syndrome
Non-tuberculous mycobacteria

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10.5588/ijtld.13.0763

Cite this

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title = "The prevalence of bronchiectasis in patients with Marfan syndrome",

abstract = "An association has been suggested between Marfan syndrome (MFS) and the nodular bronchiectatic form of lung disease caused by non-tuberculous mycobacteria (NTM). We evaluated the prevalence of bronchiectasis in 79 adult patients with MFS using computed tomography (CT) imaging. Airway dilation indicative of bronchiectasis (22/79, 28\%) and bronchioloectasis (10/79, 13\%) were relatively common, although the extent of dilation was not severe and was frequently confined to a single lobe. However, bronchiolitis was evident in only three patients (4\%), and no patient was diagnosed with NTM lung disease.",

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AU - Yi, C. A.

AU - Yoo, H.

AU - Yang, J. H.

AU - Kim, D. K.

AU - Koh, Won Jung

PY - 2014/8/1

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N2 - An association has been suggested between Marfan syndrome (MFS) and the nodular bronchiectatic form of lung disease caused by non-tuberculous mycobacteria (NTM). We evaluated the prevalence of bronchiectasis in 79 adult patients with MFS using computed tomography (CT) imaging. Airway dilation indicative of bronchiectasis (22/79, 28%) and bronchioloectasis (10/79, 13%) were relatively common, although the extent of dilation was not severe and was frequently confined to a single lobe. However, bronchiolitis was evident in only three patients (4%), and no patient was diagnosed with NTM lung disease.

AB - An association has been suggested between Marfan syndrome (MFS) and the nodular bronchiectatic form of lung disease caused by non-tuberculous mycobacteria (NTM). We evaluated the prevalence of bronchiectasis in 79 adult patients with MFS using computed tomography (CT) imaging. Airway dilation indicative of bronchiectasis (22/79, 28%) and bronchioloectasis (10/79, 13%) were relatively common, although the extent of dilation was not severe and was frequently confined to a single lobe. However, bronchiolitis was evident in only three patients (4%), and no patient was diagnosed with NTM lung disease.

KW - Bronchiectasis

KW - Marfan syndrome

KW - Non-tuberculous mycobacteria

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JO - International Journal of Tuberculosis and Lung Disease

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IS - 8

ER -

The prevalence of bronchiectasis in patients with Marfan syndrome

Abstract

UN SDGs

Keywords

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