Pleomorphic dermal sarcoma presenting in a child with Li-Fraumeni syndrome: A case report and review of the literature

Heeyeon Kim; Hyungrye Noh; Joonho Shim; Se Jin Oh; Jong Hee Lee; Dong Youn Lee; Ji Hye Park

doi:10.1111/pde.15452

Pleomorphic dermal sarcoma presenting in a child with Li-Fraumeni syndrome: A case report and review of the literature

Heeyeon Kim
, Hyungrye Noh
, Joonho Shim
, Se Jin Oh
, Jong Hee Lee
, Dong Youn Lee
, Ji Hye Park

Department of Dermatology

Research output: Contribution to journal › Article › peer-review

Abstract

Pleomorphic dermal sarcoma (PDS) is an uncommon malignant soft-tissue tumor that occurs mostly in elderly patients, with only 5% of cases occurring in children. However, pediatric patients with Li-Fraumeni syndrome (LFS) can develop several types of cancer, particularly sarcomas. Here, we describe a young LFS patient who presented with early-onset PDS and review the literature.

Original language	English
Pages (from-to)	311-314
Number of pages	4
Journal	Pediatric Dermatology
Volume	41
Issue number	2
DOIs	https://doi.org/10.1111/pde.15452
State	Published - 1 Mar 2024

UN SDGs

This output contributes to the following UN Sustainable Development Goals (SDGs)

SDG 3 Good Health and Well-being

Keywords

Li-Fraumeni syndrome (LFS)
pediatrics
sarcoma

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10.1111/pde.15452

Cite this

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title = "Pleomorphic dermal sarcoma presenting in a child with Li-Fraumeni syndrome: A case report and review of the literature",

abstract = "Pleomorphic dermal sarcoma (PDS) is an uncommon malignant soft-tissue tumor that occurs mostly in elderly patients, with only 5\% of cases occurring in children. However, pediatric patients with Li-Fraumeni syndrome (LFS) can develop several types of cancer, particularly sarcomas. Here, we describe a young LFS patient who presented with early-onset PDS and review the literature.",

keywords = "Li-Fraumeni syndrome (LFS), pediatrics, sarcoma",

author = "Heeyeon Kim and Hyungrye Noh and Joonho Shim and Oh, \{Se Jin\} and Lee, \{Jong Hee\} and Lee, \{Dong Youn\} and Park, \{Ji Hye\}",

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year = "2024",

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doi = "10.1111/pde.15452",

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AU - Kim, Heeyeon

AU - Noh, Hyungrye

AU - Shim, Joonho

AU - Oh, Se Jin

AU - Lee, Jong Hee

AU - Lee, Dong Youn

AU - Park, Ji Hye

PY - 2024/3/1

Y1 - 2024/3/1

N2 - Pleomorphic dermal sarcoma (PDS) is an uncommon malignant soft-tissue tumor that occurs mostly in elderly patients, with only 5% of cases occurring in children. However, pediatric patients with Li-Fraumeni syndrome (LFS) can develop several types of cancer, particularly sarcomas. Here, we describe a young LFS patient who presented with early-onset PDS and review the literature.

AB - Pleomorphic dermal sarcoma (PDS) is an uncommon malignant soft-tissue tumor that occurs mostly in elderly patients, with only 5% of cases occurring in children. However, pediatric patients with Li-Fraumeni syndrome (LFS) can develop several types of cancer, particularly sarcomas. Here, we describe a young LFS patient who presented with early-onset PDS and review the literature.

KW - Li-Fraumeni syndrome (LFS)

KW - pediatrics

KW - sarcoma

UR - https://www.scopus.com/pages/publications/85177754759

U2 - 10.1111/pde.15452

DO - 10.1111/pde.15452

M3 - Article

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AN - SCOPUS:85177754759

SN - 0736-8046

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SP - 311

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JO - Pediatric Dermatology

JF - Pediatric Dermatology

IS - 2

ER -

Pleomorphic dermal sarcoma presenting in a child with Li-Fraumeni syndrome: A case report and review of the literature

Abstract

UN SDGs

Keywords

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