Deep brain stimulation in a dentatorubral-pallidoluyisian atrophy patient with myoclonic dystonia

Taek Min Nam; Kyung Rae Cho; Jinyoung Youn; Jin Whan Cho; Jung Il Lee

doi:10.1016/j.jocn.2015.04.010

Deep brain stimulation in a dentatorubral-pallidoluyisian atrophy patient with myoclonic dystonia

Taek Min Nam
, Kyung Rae Cho
, Jinyoung Youn
, Jin Whan Cho
, Jung Il Lee

Department of Neurosurgery

Sungkyunkwan University

Research output: Contribution to journal › Article › peer-review

2 Scopus citations

Abstract

We describe a patient with myoclonic dystonia caused by dentatorubral-pallidoluyisian atrophy (DRPLA), which was successfully controlled with bilateral deep brain stimulation (DBS) of the globus pallidus internus (GPi). DRPLA is a rare disease which can progressively cause a loss or degeneration of neurons in the globus pallidus, dentate nucleus, subthalamic nucleus, and red nucleus. This observation is another example of secondary dystonia which can be controlled by GPi-DBS in carefully selected patients.

Original language	English
Pages (from-to)	1976-1978
Number of pages	3
Journal	Journal of Clinical Neuroscience
Volume	22
Issue number	12
DOIs	https://doi.org/10.1016/j.jocn.2015.04.010
State	Published - Dec 2015

Keywords

Deep brain stimulation
Dentatorubral-pallidoluyisian atrophy
Globus pallidus internus
Myoclonic dystonia
Secondary dystonia

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10.1016/j.jocn.2015.04.010

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title = "Deep brain stimulation in a dentatorubral-pallidoluyisian atrophy patient with myoclonic dystonia",

abstract = "We describe a patient with myoclonic dystonia caused by dentatorubral-pallidoluyisian atrophy (DRPLA), which was successfully controlled with bilateral deep brain stimulation (DBS) of the globus pallidus internus (GPi). DRPLA is a rare disease which can progressively cause a loss or degeneration of neurons in the globus pallidus, dentate nucleus, subthalamic nucleus, and red nucleus. This observation is another example of secondary dystonia which can be controlled by GPi-DBS in carefully selected patients.",

keywords = "Deep brain stimulation, Dentatorubral-pallidoluyisian atrophy, Globus pallidus internus, Myoclonic dystonia, Secondary dystonia",

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language = "English",

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AU - Nam, Taek Min

AU - Cho, Kyung Rae

AU - Youn, Jinyoung

AU - Cho, Jin Whan

AU - Lee, Jung Il

PY - 2015/12

Y1 - 2015/12

N2 - We describe a patient with myoclonic dystonia caused by dentatorubral-pallidoluyisian atrophy (DRPLA), which was successfully controlled with bilateral deep brain stimulation (DBS) of the globus pallidus internus (GPi). DRPLA is a rare disease which can progressively cause a loss or degeneration of neurons in the globus pallidus, dentate nucleus, subthalamic nucleus, and red nucleus. This observation is another example of secondary dystonia which can be controlled by GPi-DBS in carefully selected patients.

AB - We describe a patient with myoclonic dystonia caused by dentatorubral-pallidoluyisian atrophy (DRPLA), which was successfully controlled with bilateral deep brain stimulation (DBS) of the globus pallidus internus (GPi). DRPLA is a rare disease which can progressively cause a loss or degeneration of neurons in the globus pallidus, dentate nucleus, subthalamic nucleus, and red nucleus. This observation is another example of secondary dystonia which can be controlled by GPi-DBS in carefully selected patients.

KW - Deep brain stimulation

KW - Dentatorubral-pallidoluyisian atrophy

KW - Globus pallidus internus

KW - Myoclonic dystonia

KW - Secondary dystonia

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JO - Journal of Clinical Neuroscience

JF - Journal of Clinical Neuroscience

IS - 12

ER -

Deep brain stimulation in a dentatorubral-pallidoluyisian atrophy patient with myoclonic dystonia

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